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Meyer-Rocky Tansky Syndrome with A Bicornuate Uterus: A Case Report
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Mansoureh Yazdkhasti    , Bita Badehnoosh |
| Department of Gynecology & Midwifery, Faculty of Midwifery and Assistant Professor, Alborz University of Medical Sciences, Karaj, Iran , b_badehnoosh@yahoo.com |
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Abstract: (2277 Views) |
Background: Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome is an agenesis of the Müllerian system. MRKH is the second most common cause of primary amenorrhea after gonadal dysgenesis. The uterus is absent or originally formed. Only two-thirds of the vagina is formed. The ovaries are present and the karyotype is feminine and natural. Secondary sexual characteristics appear but the woman has primary amenorrhea.
Materials and Methods: This study is a case report. The patient was a 17-year-old married woman who presented with persistent and monthly pain in the abdomen and back. They have never had a menstrual cycle before. She had a bicornuate uterus and was diagnosed with MRKH. They had suffered psychological trauma due to infertility on the part of their spouse's family and were divorcing their spouse.
Results" Demographic and fertility characteristics included: age 17 years, married, BMI:21.4, age at marriage 14 years, had secondary sexual characteristics, primary amenorrhea, vaginal length three centimeters. In hormonal test AMH = 6.1, TSH = 1.57, LH = 6, Prolactin = 253.4, 17 OHProgestrone = 1.0, FSH = 5.3 were reported.
Conclusion: There are few studies in Iran on the prevalence, causes and types of Rocky Tansky syndrome. This syndrome severely reduces the quality of life of adolescent and young girls. The high cost of surgical treatment and infertility puts a lot of burden on families. It also causes a lot of psychological trauma, especially to the patient. Therefore, these people need comprehensive support. |
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| Keywords: Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome, Gonadal dysgenesis, Case report |
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Full-Text [PDF 1068 kb]
(469 Downloads)
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Type of Study: Research |
Subject:
Special
Received: 2021/10/16 | Accepted: 2021/10/02 | Published: 2021/10/02
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